A malignant tumour of breast epithelial cells
Aetiology
Risk factors
- Female sex and age are the most signigicant risk factors
- Mutations to certain genes are well-documented risk factors, most importantly the tumour suppressor genes BRCA1 and BRCA2
- Family history in a first degree relative
- Previous benign disease
- Geographic variation (more common in developed countries)
- Degree of exposure to unopposed oestrogen has also been well-documented to cause an increase in risk to develop breast cancer
- Early menarche
- Late menopause
- Nulliparous women
- First pregnancy after 30 years of age
- Oral contraceptives or HRT use
- Lifestyle factors:
- Obesity
- Physical activity is protective
- Alcohol consumption
- Diet
- NSAID lower risk
- Smoking
Pathophysiology
- Arises in the glandular epithelium of the terminal duct lobular unit (TDLU)
- It is an adenocarcinoma but is usually just referred to as ‘breast carcinoma’
Histological classification
Invasive cacinoma of the breast can be classified into:
- Invasive ductal carcinoma (75-85%)
- Can be further classified into tubular, cribriform, papillary, mucinous (/colloid), or medullary carcinomas, all showing distinct patterns of growth
- Invasive lobular carcinoma (10%)
- Characterised by a diffuse (stromal) pattern of spread that makes detection more difficult
- Other subtypes (5%), such as medullary carcinoma or colloid carcinoma
- Other factors used in classification:
- Gene expression profiling
- Hormone receptor expression - oestrogen receptor, progesterone receptor, HER2
Spread
- Local invasion - stroma of breast skin, muscles of chest wall
- Lymphatics - axillary, sentinel, apical, infraclavicular, supraclavicular, cervical, internal mammary, inframammary
- Metastasises - bone, liver, brain, lungs, abdominal viscera, female genital tract
Clinical presentation
- Patients can present symptomatically or asymptomatically via screening (particularly for ILC)
- Clinical features may include breast lump(s), asymmetry, or swelling (all or part of breast), abnormal nipple discharge, nipple retraction, skin changes (dimpling/peau d’orange, or Paget’s-like changes), mastalgia, or with a palpable lump in the axilla
Investigations
Triple assessment:
- Clinical assessment - history and breast exam
- Imaging - mammogram, breast USS
- Histology - FNA cystology C1-5 (now rarely done), core biopsy B1-5, vaccum assisted biopsy (large volume), skin biopsy, incisional biopsy of mass (now rare)
- Grading - tubular differentiation, nuclear pleomorphism, mitotic activity
- Staging - TNM
Management
Breast conserving surgery
- Breast conserving surgery is the preferred treatment - wide local excision with or without an oncoplastic procedure to shape the breast
Modified radical mastectomy
- Removes the entire breast, including the overlying skin and axillary lymph nodes
- Pectoralis major muscle is preserved - facilitates wound healing and potentially allows for reconstruction
- Most women who require or request mastectomy are candidates for breast reconsturction - prosthetic or autologous tissue
Axillary surgery
- Axillary surgery is most commonly performed alongside wide local excision and mastectomies, in order to assess nodal status (SNB) and remove any nodal disease
- Axillary node clearance involves removing all nodes in the axilla - common complications include paraesthesia, seroma formation, and lymphedema in the upper limb
Radiation therapy
- Essential component of breast-conserving surgery
- Indications for post-mastectomy RT include involvement of more than three nodes, positive surgical margins and/or tumors larger than 5 cm
Adjuvant systemic therapy
- Chemotherapy
- Hormonal therapy
- Tamoxifen used typically in pre-menopausal patients
- Aromatase inhibitors are advised for post-menopausal patients as adjuvant therapy
- Immunotherapy may be used in patients whose cancers express specific growth factor receptors
- Herceptin for HER-2
- Bevacizuman for VEGF
- Lapatibin for EGFR and HER-2