Spectrum of conditions that affect a woman's endocrine system, which controls her hormones and her patterns of ovulation
Aetiology
Group I: hypothalamic pituitary failure
- Account for 10% of ovulatory disorders
- Amenorrhoea
- Low levels of FSH/LH
- Oestrogen deficiency - negative progesterone challenge test
- Hypogonadotrophic hypogonadism
Causes
- Stress
- Excessive exercise
- Anorexia/low BMI
- Brain/pituitary tumours
- Head trauma
- Kallman's syndrome
- Drugs (steriods, opiates)
Group II: hypothalamic pituitary dysfunction
- Accounts for 85% of ovulatory disorders
- Oligo/amenorrhoea
- Normal gonadotrophins/excess LH
- Normal oestrogen levels
- Nearly always PCOS
- 10-20% amenorrhoea
- 80-90% oligomenorrhoea
Group III: ovarian failure
- Accounts for 5% of ovulatory disorders
- Amenorrhoic patients who are menopausal
- High levels gonadotrophins - raised FSH>30 IU/l x 2 samples
- Low oestrogen levels
Premature ovarian failure
- Defined as menopause before 40 years
- Causes include genetic e.g. Turner syndrome, autoimmune ovarian failure, bilateral oophrectomy, pelvic radio/chemotherapy
Hyperprolactinaemia
- Should also be considered
Pathophysiology
- Menstrual bleeding usually lasts < 5 days
- Ovulatory disorders are associated with oligomenorrhea and amenorrhea
- Oligomenorrhoea: cycles > 42 days (< 8 periods/year)
- Amenorrhea: absent mentration, can be primary (never mentruated) or secondary (mentruation started then stop)
Investigations
Assessing ovulation
- Regular cycles are highly suggestive of ovulation - confirm by midluteal (D21) serum progesterone (> 30 nmol/l) x 2 samples
- Irregular cycles are probably anovulatory - needs hormone evaluation (FSH, LH, TSH, prolactin, oestragiol, testosterone, SHBG, FAI)
Progesterone challenge test
- Involves administration of progesterone to induce a period - provera 5mg BD x 5 days
- Withdrawal bleed usually within 7-10 days after progesterone, this would indicate that oestrogen levels are normal
- If no bleeding - low oestrogen levels, uterine/endometrial abnormality or cervical stenosis
Ultrasound
- Transvaginal
- Examines pelvic anatomy - uterus, PCOS
- Scans to look for follicular growth/monitor ovulation induction
Others
- Karyotype
- Autoantibody screen
- MRI of pituitary
- Bone density scan
Management of infertility caused by ovulation disorders
Pre-fertility treatment
- Stabilise weight - BMI >18.5 and <30
- Lifestyle modification - smoking, alcohol
- Folic acid 400 mcg daily, 5mg daily if BMI over 30
- Check prescribed drugs
- Check rubella immunity
- Normal semen analysis
- Patent fallopian tube
Management of type I anovulation
- Stabilise weight (BMI > 18.5)
- Pulsatile GNRH (SC/IV pump worn continuously) OR gonadrotrophin (FSH + LH) daily injections
- Gonadrotrophin daily injections have higher multiple pregnancy rates
- Both need ultrasound monitoring of response (follicle tracking)
Management of type II anovulation (PCOS)
- Lifestyle - 90% of women with PCOS are obese, only induce ovulation when BMI under 30
- First line - clomifene citrate (PO)
- Alternatively - tamoxifen, letrozole
- In patients who do not respond to clomifene citrate, consider metformin - reduces insulin resistance and androgens so can restore mentruation/ovulation; may increase pregnancy rate and may improve sensitivity to clomifene
- If fails: gonadotrophin therapy - daily recombinent FSH injections
- Risk of multiple pregnancy or overstimulation
- If fails: laparoscopic ovarian diathermy
- Mainly singleton pregnancies
- Risks: risks associated with general anaethetic and laparoscopic procedures, ovarian destruction
- Last line: IVF
Management of premature ovarian failure
- Hormone replacement therapy
- Egg/embryo donation
- Ovary/egg/embryo cryopreservation prior to chemo/radiotherapy where POF anticipated
- Counselling/support network