Photosensitivity describes a group of skin disorders that result from exposure to normal levels of UV light exposure
Fitzpatrick skin types
Normal human skin is photosensitive in that it reddens/tans following following acute sunlight exposure, and thickens following chronic sunlight exposure
Photosensivity is multi-factorial with it being influenced by the intensity of UV light, genetics, genetics, drugs and skin types
Xeroderma pigmentosum
Xeroderma pigmentosum refers to a group of autosomal recessive genetic disorders caused by a deficiency in the DNA repair mechanisms in the skin
Clinical presentation
Severe photosensitivity
Accelerated photo ageing
Ocular damage
Early formation of skin cancers
Management
Patients are required to undertake strict sun avoidance
Most will die in teenage or early adult years due to skin cancer